Protein detail

ABCC9

ATP-binding cassette sub-family C member 9 (Sulfonylurea receptor 2)

Protein symbol
ABCC9
UniProt ID
EVMP score
0.50
Frequency
1
Transmembrane count
15
Protein classification
Disease related genesFDA approved drug targetsHuman disease related genesMetabolic proteinsPredicted membrane proteinsTransporters
EVMP score: annotation confidence score.
Extremely high >= 0.85High >= 0.70Medium >= 0.55Low >= 0.40
Basic Information
Protein Names
ATP-binding cassette sub-family C member 9 (Sulfonylurea receptor 2)
Protein Class
Disease related genesFDA approved drug targetsHuman disease related genesMetabolic proteinsPredicted membrane proteinsTransporters
Protein Function
  • Disease related genes
  • Human disease related genes:Cardiovascular diseases:Cardiac diseases
  • Transporters:Primary Active Transporters
  • FDA approved drug targets:Small molecule drugs
Transmembrane
31..51; Helical; Name=1; 73..93; Helical; Name=2; 102..122; Helical; Name=3; 133..153; Helical; Name=4; 168..188; Helical; Name=5; 302..322; Helical; Name=6; 351..371; Helical; Name=7; 424..444; Helical; Name=8; 456..476; Helical; Name=9; 532..552; Helical; Name=10; 572..592; Helical; Name=11; 991..1011; Helical; Name=12; 1035..1055; Helical; Name=13; 1128..1148; Helical; Name=14; 1246..1266; Helical; Name=15
Transmembrane Count
15
Entrez Gene Symbol
Gene Synonym
CMD1OSUR2
Gene Description
ATP binding cassette subfamily C member 9
Chromosome
12
Position
21797389-21942543
Frequency
1
EVMP Score
0.50
Fluorescence & Localization
Cell SpecificEndometrial glandular cellsBlood Cell Specificplasmacytoid DC
Function & Pathway
Protein Function
  • Disease related genes
  • Human disease related genes:Cardiovascular diseases:Cardiac diseases
  • Transporters:Primary Active Transporters
  • FDA approved drug targets:Small molecule drugs
Mediation Categories
Clinical-translation mediationFusion and delivery mediationImmune mediationMetabolism mediation
Relations & Evidence

Enzyme-Mediated Modification

0 records.

Ligand-Receptor Signaling

26 records.

CategoryParentDatabaseTransmitterReceiverSecretedPlasma Membrane (Transmembrane)Plasma Membrane (Peripheral)
receptorreceptorOmniPathNoYesNoNoNo
intracellularintracellularLOCATENoNoNoNoNo
intracellularintracellularComPPINoNoNoNoNo
intracellularintracellularGO_IntercellNoNoNoNoNo
intracellularintracellularOmniPathNoNoNoNoNo
transportertransporterSurfaceomeNoYesNoNoNo
abcctransporterHGNCNoYesNoNoNo
transportertransporterHGNCNoYesNoNoNo
abctransporterDGIdbNoYesNoNoNo
transportertransporterDGIdbNoYesNoNoNo
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Regulatory Interaction Network

0 records.

Protein Complex Composition

3 records.

Component NameComponent Gene SymbolsComponent UniProt IDStoichiometryDatabaseDatabase IDsReferences
KATP channelABCC8ABCC9KCNJ11KCNJ8O60706Q09428Q14654Q158420:0:0:0SIGNORSIGNOR:SIGNOR-C274
KCNJ11-ABCC9 complexABCC9KCNJ11O60706Q146541:1CORUMComplexPortalCORUM:6654intact:EBI-10954853intact:EBI-10954742983170825236767200860791475529218079561190795619382894
ABCC9ATP13A1CYP26C1FA2HGOLT1BKCNJ11REEP3SACM1LSURF4TMED10TMED2TMED7TMED9UBCURGCPO15260O60706P0CG48P49755Q14654Q15363Q6NUK4Q6V0L0Q7L5A8Q8TCY9Q9BVK6Q9HD20Q9NTJ5Q9Y3B3Q9Y3E01:1:1:1:1:1:1:1:1:1:1:1:1:1:1NetworkBlastCompleatCompleat:HC7240

Isolation & Detection Technology

1 record.

EV Isolation MethodDetection MethodNumber of ReferencesReferences
Differential UltracentrifugationMass spectrometry131805958
Sequence, Structure & Domains

Sequences

Length
1,549
Mass
174,223
Sequence
MSLSFCGNNISSYNINDGVLQNSCFVDALNLVPHVFLLFITFPILFIGWGSQSSKVQIHHNTWLHFPGHNLRWILTFALLFVHVCEIAEGIVSDSRRESRHLHLFMPAVMGFVATTTSIVYYHNIETSNFPKLLLALFLYWVMAFITKTIKLVKYCQSGLDISNLRFCITGMMVILNGLLMAVEINVIRVRRYVFFMNPQKVKPPEDLQDLGVRFLQPFVNLLSKATYWWMNTLIISAHKKPIDLKAIGKLPIAMRAVTNYVCLKDAYEEQKKKVADHPNRTPSIWLAMYRAFGRPILLSSTFRYLADLLGFAGPLCISGIVQRVNETQNGTNNTTGISETLSSKEFLENAYVLAVLLFLALILQRTFLQASYYVTIETGINLRGALLAMIYNKILRLSTSNLSMGEMTLGQINNLVAIETNQLMWFLFLCPNLWAMPVQIIMGVILLYNLLGSSALVGAAVIVLLAPIQYFIATKLAEAQKSTLDYSTERLKKTNEILKGIKLLKLYAWEHIFCKSVEETRMKELSSLKTFALYTSLSIFMNAAIPIAAVLATFVTHAYASGNNLKPAEAFASLSLFHILVTPLFLLSTVVRFAVKAIISVQKLNEFLLSDEIGDDSWRTGESSLPFESCKKHTGVQPKTINRKQPGRYHLDSYEQSTRRLRPAETEDIAIKVTNGYFSWGSGLATLSNIDIRIPTGQLTMIVGQVGCGKSSLLLAILGEMQTLEGKVHWSNVNESEPSFEATRSRNRYSVAYAAQKPWLLNATVEENITFGSPFNKQRYKAVTDACSLQPDIDLLPFGDQTEIGERGINLSGGQRQRICVARALYQNTNIVFLDDPFSALDIHLSDHLMQEGILKFLQDDKRTLVLVTHKLQYLTHADWIIAMKDGSVLREGTLKDIQTKDVELYEHWKTLMNRQDQELEKDMEADQTTLERKTLRRAMYSREAKAQMEDEDEEEEEEEDEDDNMSTVMRLRTKMPWKTCWRYLTSGGFFLLILMIFSKLLKHSVIVAIDYWLATWTSEYSINNTGKADQTYYVAGFSILCGAGIFLCLVTSLTVEWMGLTAAKNLHHNLLNKIILGPIRFFDTTPLGLILNRFSADTNIIDQHIPPTLESLTRSTLLCLSAIGMISYATPVFLVALLPLGVAFYFIQKYFRVASKDLQELDDSTQLPLLCHFSETAEGLTTIRAFRHETRFKQRMLELTDTNNIAYLFLSAANRWLEVRTDYLGACIVLTASIASISGSSNSGLVGLGLLYALTITNYLNWVVRNLADLEVQMGAVKKVNSFLTMESENYEGTMDPSQVPEHWPQEGEIKIHDLCVRYENNLKPVLKHVKAYIKPGQKVGICGRTGSGKSSLSLAFFRMVDIFDGKIVIDGIDISKLPLHTLRSRLSIILQDPILFSGSIRFNLDPECKCTDDRLWEALEIAQLKNMVKSLPGGLDAVVTEGGENFSVGQRQLFCLARAFVRKSSILIMDEATASIDMATENILQKVVMTAFADRTVVTIAHRVSSIMDAGLVLVFSEGILVECDTVPNLLAHKNGLFSTLVMTNK
Alternative Products
Event=Alternative splicing; Named isoforms=2; Name=SUR2A; IsoId=O60706-1; Sequence=Displayed; Name=SUR2B; IsoId=O60706-2; Sequence=VSP_000058
Alternative Sequence
1508..1549; SSIMDAGLVLVFSEGILVECDTVPNLLAHKNGLFSTLVMTNK -> HTILTADLVIVMKRGNILEYDTPESLLAQENGVFASFVRADM (in isoform SUR2B)

3D Structural Models

Domain & Motif Annotations

Compositional Bias
951..966; Acidic residues
Domain (FT)
297..597; ABC transmembrane type-1 1; 672..912; ABC transporter 1; 994..1274; ABC transmembrane type-1 2; 1312..1546; ABC transporter 2
Region
944..967; Disordered
Protein Families
  • ABC transporter superfamily
  • ABCC family
  • Conjugate transporter (TC 3.A.1.208) subfamily
Sequence Similarities
Belongs to the ABC transporter superfamily. ABCC family. Conjugate transporter (TC 3.A.1.208) subfamily.
Clinical Relevance
Disease Involvement
Atrial fibrillationCardiomyopathyDisease variantFDA approved drug targetsIntellectual disability
Biomarker
Approved; Discontinued in Phase 1
Drug Targets
FDA approved drug targets
Antibody