Protein detail

ATS2

A disintegrin and metalloproteinase with thrombospondin motifs 2 (ADAM-TS 2) (ADAM-TS2) (ADAMTS-2) (EC 3.4.24.14) (Procollagen I N-proteinase) (PC I-NP) (Procollagen I/II amino propeptide-processing enzyme) (Procollagen N-endopeptidase) (pNPI)

Entry name
ATS2
UniProt ID
EVMP score
0.38
Frequency
1
Transmembrane count
Protein classification
Disease related genesEnzymesHuman disease related genesPlasma proteinsPotential drug targetsPredicted secreted proteins
EVMP score: annotation confidence score.
Extremely high >= 0.85High >= 0.70Medium >= 0.55Low >= 0.40
Basic Information
Protein Names
A disintegrin and metalloproteinase with thrombospondin motifs 2 (ADAM-TS 2) (ADAM-TS2) (ADAMTS-2) (EC 3.4.24.14) (Procollagen I N-proteinase) (PC I-NP) (Procollagen I/II amino propeptide-processing enzyme) (Procollagen N-endopeptidase) (pNPI)
Protein Class
Disease related genesEnzymesHuman disease related genesPlasma proteinsPotential drug targetsPredicted secreted proteins
Protein Function
  • Potential drug targets
  • Enzymes
  • Predicted secreted proteins
  • Human disease related genes:Congenital malformations:Congenital malformations of skin
  • ENZYME proteins:Hydrolases
  • Disease related genes
Entrez Gene Symbol
Gene Synonym
ADAM-TS2ADAMTS-3hPCPNINPIPCINP
Gene Description
ADAM metallopeptidase with thrombospondin type 1 motif 2
Chromosome
5
Position
179110853-179345461
Frequency
1
EVMP Score
0.38
Fluorescence & Localization
Tissue SpecificprostateCell SpecificAlveolar cells type 2Single-Nuclei Brain Specificchoroid plexus epithelial cellSecretome LocationSecreted in other tissuesSecretome FunctionEnzyme
Function & Pathway
Relations & Evidence

Enzyme-Mediated Modification

0 records.

Ligand-Receptor Signaling

22 records.

CategoryParentDatabaseTransmitterReceiverSecretedPlasma Membrane (Transmembrane)Plasma Membrane (Peripheral)
secretedsecretedOmniPathNoNoYesNoNo
receptorreceptorscConnectNoYesYesNoNo
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Regulatory Interaction Network

0 records.

Protein Complex Composition

0 records.

Isolation & Detection Technology

1 record.

EV Isolation MethodDetection MethodNumber of ReferencesReferences
Differential UltracentrifugationSize Exclusion ChromatographyMass spectrometry3257551793801459537223008
Sequence, Structure & Domains

Sequences

Length
1,211
Mass
134,755
Sequence
MDPPAGAARRLLCPALLLLLLLLPPPLLPPPPPPANARLAAAADPPGGPLGHGAERILAVPVRTDAQGRLVSHVVSAATSRAGVRARRAAPVRTPSFPGGNEEEPGSHLFYNVTVFGRDLHLRLRPNARLVAPGATMEWQGEKGTTRVEPLLGSCLYVGDVAGLAEASSVALSNCDGLAGLIRMEEEEFFIEPLEKGLAAQEAEQGRVHVVYRRPPTSPPLGGPQALDTGASLDSLDSLSRALGVLEEHANSSRRRARRHAADDDYNIEVLLGVDDSVVQFHGKEHVQKYLLTLMNIVNEIYHDESLGAHINVVLVRIILLSYGKSMSLIEIGNPSQSLENVCRWAYLQQKPDTGHDEYHDHAIFLTRQDFGPSGMQGYAPVTGMCHPVRSCTLNHEDGFSSAFVVAHETGHVLGMEHDGQGNRCGDEVRLGSIMAPLVQAAFHRFHWSRCSQQELSRYLHSYDCLLDDPFAHDWPALPQLPGLHYSMNEQCRFDFGLGYMMCTAFRTFDPCKQLWCSHPDNPYFCKTKKGPPLDGTMCAPGKHCFKGHCIWLTPDILKRDGSWGAWSPFGSCSRTCGTGVKFRTRQCDNPHPANGGRTCSGLAYDFQLCSRQDCPDSLADFREEQCRQWDLYFEHGDAQHHWLPHEHRDAKERCHLYCESRETGEVVSMKRMVHDGTRCSYKDAFSLCVRGDCRKVGCDGVIGSSKQEDKCGVCGGDNSHCKVVKGTFTRSPKKHGYIKMFEIPAGARHLLIQEVDATSHHLAVKNLETGKFILNEENDVDASSKTFIAMGVEWEYRDEDGRETLQTMGPLHGTITVLVIPVGDTRVSLTYKYMIHEDSLNVDDNNVLEEDSVVYEWALKKWSPCSKPCGGGSQFTKYGCRRRLDHKMVHRGFCAALSKPKAIRRACNPQECSQPVWVTGEWEPCSQTCGRTGMQVRSVRCIQPLHDNTTRSVHAKHCNDARPESRRACSRELCPGRWRAGPWSQCSVTCGNGTQERPVLCRTADDSFGICQEERPETARTCRLGPCPRNISDPSKKSYVVQWLSRPDPDSPIRKISSKGHCQGDKSIFCRMEVLSRYCSIPGYNKLCCKSCNLYNNLTNVEGRIEPPPGKHNDIDVFMPTLPVPTVAMEVRPSPSTPLEVPLNASSTNATEDHPETNAVDEPYKIHGLEDEVQPPNLIPRRPSPYEKTRNQRIQELIDEMRKKEMLGKF
Alternative Products
Event=Alternative splicing; Named isoforms=2; Name=LpNPI; IsoId=O95450-1; Sequence=Displayed; Name=SpNPI; IsoId=O95450-2; Sequence=VSP_005497, VSP_005498
Alternative Sequence
544..566; HCFKGHCIWLTPDILKRDGSWGA -> FRPGAVAHACYPSTLGGQGRWIA (in isoform SpNPI); 567..1211; Missing (in isoform SpNPI)

3D Structural Models

Domain & Motif Annotations

Motif
691..693; Cell attachment site
Domain (CC)
The spacer domain and the TSP type-1 domains are important for a tight interaction with the extracellular matrix.
Domain (FT)
266..470; Peptidase M12B; 480..560; Disintegrin; 561..616; TSP type-1 1; 854..912; TSP type-1 2; 914..971; TSP type-1 3; 975..1029; TSP type-1 4; 1059..1097; PLAC
Region
723..851; Spacer; 1170..1191; Disordered
Clinical Relevance
Disease Involvement
Ehlers-Danlos syndrome