Protein detail

CLCN5

H(+)/Cl(-) exchange transporter 5 (Chloride channel protein 5) (ClC-5) (Chloride transporter ClC-5)

Protein symbol
CLCN5
UniProt ID
EVMP score
0.50
Frequency
3
Transmembrane count
10
Protein classification
Disease related genesHuman disease related genesPlasma proteinsPotential drug targetsPredicted intracellular proteinsPredicted membrane proteinsTransporters
Basic Information
Protein Names
H(+)/Cl(-) exchange transporter 5 (Chloride channel protein 5) (ClC-5) (Chloride transporter ClC-5)
Protein Class
Disease related genesHuman disease related genesPlasma proteinsPotential drug targetsPredicted intracellular proteinsPredicted membrane proteinsTransporters
Protein Function
  • Human disease related genes:Urinary system diseases:Kidney diseases
  • Predicted intracellular proteins
  • Human disease related genes:Congenital disorders of metabolism:Congenital disorders of ion transport and metabolism
  • Potential drug targets
  • Transporters:Electrochemical Potential-driven transporters
  • Disease related genes
Transmembrane
125..162; Helical; 208..231; Helical; 256..275; Helical; 281..300; Helical; 348..366; Helical; 389..415; Helical; 422..442; Helical; 498..518; Helical; 523..542; Helical; 605..622; Helical
Transmembrane Count
10
Entrez Gene Symbol
Gene Synonym
ClC-5CLC5DENTShCIC-K2hClC-K2NPHL1NPHL2XLRHXRN
Gene Description
Chloride voltage-gated channel 5
Chromosome
X
Position
49922596-50099235
Frequency
3
EVMP Score
0.50
Fluorescence & Localization
Tissue Specificheart muscleCell SpecificCone photoreceptor cellsBlood Cell Specificplasmacytoid DCBlood Lineage Specificdendritic cells
Function & Pathway
Relations & Evidence

Enzyme-Mediated Modification

0 records.

Ligand-Receptor Signaling

24 records.

CategoryParentDatabaseTransmitterReceiverSecretedPlasma Membrane (Transmembrane)Plasma Membrane (Peripheral)
receptorreceptorOmniPathNoYesNoNoNo
intracellularintracellularLOCATENoNoNoNoNo
intracellularintracellularComPPINoNoNoNoNo
intracellularintracellularGO_IntercellNoNoNoNoNo
intracellularintracellularUniProt_locationNoNoNoNoNo
intracellularintracellularOmniPathNoNoNoNoNo
ion_channelion_channelDGIdbNoYesNoNoNo
ion_channelion_channelAlmen2009NoYesNoNoNo
voltage_gated_chlorideion_channelAlmen2009NoYesNoNoNo
transportertransporterOmniPathNoYesNoNoNo
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Regulatory Interaction Network

1 record.

Source Protein SymbolSource UniProt IDTarget Protein SymbolTarget UniProt IDIs DirectedIs StimulationIs InhibitionDatabaseReferences
NED4LQ96PU5CLCN5P51795YesNoYesSIGNORSIGNOR:15489223

Protein Complex Composition

5 records.

Component NameComponent Gene SymbolsComponent UniProt IDStoichiometryDatabaseDatabase IDsReferences
HT_DM_Cluster393CLCN3CLCN4CLCN5TMEM9TMEM9BP51790P51793P51795Q9NQ34Q9P0T71:1:1:1:1CompleatCompleat:HC280222036573
CLCN5RUFY1RUFY2SERPINB7O75635P51795Q8WXA3Q96T510:0:0:0hu.MAP2
ADGRG5CLCN3CLCN5TMEM9BP51790P51795Q8IZF4Q9NQ340:0:0:0hu.MAP2
CLCN5P517956PDBPDB:2j9lPDB:2ja3
CLCN5TMEM9BP51795Q9NQ340:0hu.MAP2

Isolation & Detection Technology

1 record.

EV Isolation MethodDetection MethodNumber of ReferencesReferences
Differential UltracentrifugationSize Exclusion ChromatographyMass spectrometry127605433
Sequence, Structure & Domains

Sequences

Length
816
Mass
90,785
Sequence
MAMWQGAMDNRGFQQGSFSSFQNSSSDEDLMDIPATAMDFSMRDDVPPLDREVGEDKSYNGGGIGSSNRIMDFLEEPIPGVGTYDDFNTIDWVREKSRDRDRHREITNKSKESTWALIHSVSDAFSGWLLMLLIGLLSGSLAGLIDISAHWMTDLKEGICTGGFWFNHEHCCWNSEHVTFEERDKCPEWNSWSQLIISTDEGAFAYIVNYFMYVLWALLFAFLAVSLVKVFAPYACGSGIPEIKTILSGFIIRGYLGKWTLVIKTITLVLAVSSGLSLGKEGPLVHVACCCGNILCHCFNKYRKNEAKRREVLSAAAAAGVSVAFGAPIGGVLFSLEEVSYYFPLKTLWRSFFAALVAAFTLRSINPFGNSRLVLFYVEFHTPWHLFELVPFILLGIFGGLWGALFIRTNIAWCRKRKTTQLGKYPVIEVLVVTAITAILAFPNEYTRMSTSELISELFNDCGLLDSSKLCDYENRFNTSKGGELPDRPAGVGVYSAMWQLALTLILKIVITIFTFGMKIPSGLFIPSMAVGAIAGRLLGVGMEQLAYYHQEWTVFNSWCSQGADCITPGLYAMVGAAACLGGVTRMTVSLVVIMFELTGGLEYIVPLMAAAMTSKWVADALGREGIYDAHIRLNGYPFLEAKEEFAHKTLAMDVMKPRRNDPLLTVLTQDSMTVEDVETIISETTYSGFPVVVSRESQRLVGFVLRRDLIISIENARKKQDGVVSTSIIYFTEHSPPLPPYTPPTLKLRNILDLSPFTVTDLTPMEIVVDIFRKLGLRQCLVTHNGRLLGIITKKDVLKHIAQMANQDPDSILFN
Alternative Products
Event=Alternative splicing; Named isoforms=2; Name=1; IsoId=P51795-2; Sequence=Displayed; Name=2; IsoId=P51795-1; Sequence=VSP_060654
Alternative Sequence
1..70; Missing (in isoform 2)

3D Structural Models

Turn
696..698
Helix
652..655; 675..684; 707..718; 750..752; 766..776; 795..805
Beta Strand
656..658; 668..671; 688..694; 700..706; 729..731; 733..735; 753..756; 759..761; 779..785; 788..794
3D Structure
X-ray crystallography (2)

Domain & Motif Annotations

Compositional Bias
12..25; Low complexity
Motif
237..241; Selectivity filter part_1; 279..283; Selectivity filter part_2; 523..527; Selectivity filter part_3
Domain (FT)
656..720; CBS 1; 752..812; CBS 2
Region
1..26; Disordered
Protein Families
  • Chloride channel (TC 2.A.49) family
  • ClC-5/CLCN5 subfamily
Sequence Similarities
Belongs to the chloride channel (TC 2.A.49) family. ClC-5/CLCN5 subfamily.
Clinical Relevance
Disease Involvement
Disease variant
Drug Targets
Literature-reported targetSuccessful target
Interaction Protein
ENSG00000116857ENSG00000175348
Interaction Count
2
Interaction Dataset
biogrid_bioplex