Protein detail

RAGE

Advanced glycosylation end product-specific receptor (Receptor for advanced glycosylation end products)

Entry name
RAGE
UniProt ID
EVMP score
0.50
Frequency
1
Transmembrane count
1
Protein classification
Cancer-related genesPlasma proteinsPredicted membrane proteinsPredicted secreted proteinsTransporters
EVMP score: annotation confidence score.
Extremely high >= 0.85High >= 0.70Medium >= 0.55Low >= 0.40
Basic Information
Protein Names
Advanced glycosylation end product-specific receptor (Receptor for advanced glycosylation end products)
Protein Class
Cancer-related genesPlasma proteinsPredicted membrane proteinsPredicted secreted proteinsTransporters
Protein Function
  • Cancer-related genes:Candidate cancer biomarkers
  • Predicted secreted proteins
  • Transporters:Accessory Factors Involved in Transport
Transmembrane
343..363; Helical
Transmembrane Count
1
Entrez Gene Symbol
Gene Synonym
RAGESCARJ1sRAGE
Gene Description
Advanced glycosylation end-product specific receptor
Chromosome
6
Position
32180968-32184322
Frequency
1
EVMP Score
0.50
Fluorescence & Localization
Tissue Specificskeletal muscleCell SpecificFoveolar cellsSingle-Nuclei Brain Specificcentral nervous system macrophage
Function & Pathway
Protein Function
  • Cancer-related genes:Candidate cancer biomarkers
  • Predicted secreted proteins
  • Transporters:Accessory Factors Involved in Transport
Canonical Pathways
M90 Pid wnt canonical pathway
Mediation Categories
Adhesion and uptake mediationClinical-translation mediationFusion and delivery mediationImmune mediationMetabolism mediationReceptor-signaling mediation
Relations & Evidence

Enzyme-Mediated Modification

2 records.

Substrate Gene SymbolEnzyme Gene SymbolEnzyme UniProt IDResidue TypeResidue OffsetModificationDatabaseReferences
AGERATMQ13315S391phosphorylationSparser_ProtMapperProtMapperREACH_ProtMapperPhosphoSitePhosphoSite_ProtMapperProtMapper:28977635
AGERPRKCZQ05513S391phosphorylationPhosphoSite

Ligand-Receptor Signaling

41 records.

CategoryParentDatabaseTransmitterReceiverSecretedPlasma Membrane (Transmembrane)Plasma Membrane (Peripheral)
receptorreceptorGO_IntercellNoYesYesYesNo
receptorreceptorCellTalkDBNoYesYesYesNo
receptorreceptorSurfaceomeNoYesYesYesNo
igreceptorSurfaceomeNoYesYesYesNo
receptorreceptorOmniPathNoYesYesYesNo
extracellularextracellularLOCATENoNoYesYesNo
extracellularextracellularOmniPathNoNoYesYesNo
intracellularintracellularLOCATENoNoYesYesNo
intracellularintracellularComPPINoNoYesYesNo
intracellularintracellularGO_IntercellNoNoYesYesNo
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Regulatory Interaction Network

6 records.

Source Protein SymbolSource UniProt IDTarget Protein SymbolTarget UniProt IDIs DirectedIs StimulationIs InhibitionDatabaseReferences
S10A8P05109RAGEQ15109YesYesNoCellinkerCellTalkDBSIGNORCellinker:28504650CellTalkDB:28504650SIGNOR:28137827
ATMQ13315RAGEQ15109YesYesNoSparser_ProtMapperSIGNORProtMapperREACH_ProtMapperPhosphoSite_ProtMapperProtMapper:28977635SIGNOR:28977635
HMGB1P09429RAGEQ15109YesYesNoCellTalkDBSparser_ProtMapperSIGNORProtMapperHPRDHINTInnateDBCellinkerWangHPRD:9812979Cellinker:20192808HINT:24474694InnateDB:19727205SIGNOR:25014009CellTalkDB:32296583
COMPLEX:P05109_P06702RAGEQ15109YesYesNoSIGNORSIGNOR:28137827
S10A9P06702RAGEQ15109YesYesNoInnateDBCellinkerCellTalkDBSIGNORCellinker:28504650InnateDB:23667563CellTalkDB:28504650SIGNOR:28137827
KPCZQ05513RAGEQ15109YesNoNoProtMapperIntActInnateDBPhosphoSitePhosphoSite_ProtMapperPhosphoSite:25002577IntAct:21829704PhosphoSite:21829704InnateDB:21829704

Protein Complex Composition

4 records.

Component NameComponent Gene SymbolsComponent UniProt IDStoichiometryDatabaseDatabase IDsReferences
AGERS100BP04271Q151094:1PDBPDB:4xynPDB:5d7f
AGERHMGB1P09429Q151091:1PDBPDB:8i9m
AGERS100PP25815Q151092:2PDBPDB:2mjw
AGERQ151092PDBPDB:6xq8PDB:6xq1PDB:7lmwPDB:4ofvPDB:6xq3PDB:6xq5PDB:6xq7PDB:4oi7PDB:4lp5PDB:4lp4PDB:6xq9PDB:7lmlPDB:4of5PDB:6xq6PDB:4oi8

Isolation & Detection Technology

1 record.

EV Isolation MethodDetection MethodNumber of ReferencesReferences
Differential UltracentrifugationSize Exclusion ChromatographyWestern blotting132560723
Sequence, Structure & Domains

Sequences

Length
404
Mass
42,803
Sequence
MAAGTAVGAWVLVLSLWGAVVGAQNITARIGEPLVLKCKGAPKKPPQRLEWKLNTGRTEAWKVLSPQGGGPWDSVARVLPNGSLFLPAVGIQDEGIFRCQAMNRNGKETKSNYRVRVYQIPGKPEIVDSASELTAGVPNKVGTCVSEGSYPAGTLSWHLDGKPLVPNEKGVSVKEQTRRHPETGLFTLQSELMVTPARGGDPRPTFSCSFSPGLPRHRALRTAPIQPRVWEPVPLEEVQLVVEPEGGAVAPGGTVTLTCEVPAQPSPQIHWMKDGVPLPLPPSPVLILPEIGPQDQGTYSCVATHSSHGPQESRAVSISIIEPGEEGPTAGSVGGSGLGTLALALGILGGLGTAALLIGVILWQRRQRRGEERKAPENQEEEEERAELNQSEEPEAGESSTGGP
Alternative Products
Event=Alternative splicing; Named isoforms=10; Name=1; IsoId=Q15109-1; Sequence=Displayed; Name=2; Synonyms=RAGESEC; IsoId=Q15109-2; Sequence=VSP_002551, VSP_002552; Name=3; IsoId=Q15109-3; Sequence=VSP_042011; Name=4; IsoId=Q15109-4; Sequence=VSP_043528, VSP_042011; Name=5; Synonyms=del exon3-7; IsoId=Q15109-5; Sequence=VSP_047884, VSP_047885; Name=6; IsoId=Q15109-6; Sequence=VSP_043528; Name=7; Synonyms=del exon3; IsoId=Q15109-7; Sequence=VSP_002551; Name=8; IsoId=Q15109-8; Sequence=VSP_047886, VSP_047888; Name=9; Synonyms=del exon8-9; IsoId=Q15109-9; Sequence=VSP_047887, VSP_047889; Name=10; Synonyms=delta-ICD, variant 20; IsoId=Q15109-10; Sequence=VSP_055321
Alternative Sequence
54..67; Missing (in isoform 2 and isoform 7); 113..121; YRVRVYQIP -> WWWSQKVEQ (in isoform 5); 122..404; Missing (in isoform 5); 140; K -> KVVEESRRSRKRPCEQE (in isoform 4 and isoform 6); 275..404; GVPLPLPPSPVLILPEIGPQDQGTYSCVATHSSHGPQESRAVSISIIEPGEEGPTAGSVGGSGLGTLALALGILGGLGTAALLIGVILWQRRQRRGEERKAPENQEEEEERAELNQSEEPEAGESSTGGP -> VSDLERGAGRTRRGGANCRLCGRIRAGNSSPGPGDPGRPGDSRPAHWGHLVAKAATPRRGEEGPRKPGGRGGACRTESVGGT (in isoform 2); 275..325; GVPLPLPPSPVLILPEIGPQDQGTYSCVATHSSHGPQESRAVSISIIEPGE -> NQARRGQLQVRGLIKSGKQKIAPNTCDWGDGQQERNGRPQKTRRKRRSVQN (in isoform 8); 276..355; VPLPLPPSPVLILPEIGPQDQGTYSCVATHSSHGPQESRAVSISIIEPGEEGPTAGSVGGSGLGTLALALGILGGLGTAA -> LRTREPTAVWPPIPATGPRKAVLSASASSNQARRGQLQVRGLIKSGKQKIAPNTCDWGDGQQERNGRPQKTRRKRRSVQN (in isoform 9); 326..404; Missing (in isoform 8); 332..404; SVGGSGLGTLALALGILGGLGTAALLIGVILWQRRQRRGEERKAPENQEEEEERAELNQSEEPEAGESSTGGP -> EGFDKVREAEDSPQHM (in isoform 3 and isoform 4); 356..404; Missing (in isoform 9); 374..404; KAPENQEEEEERAELNQSEEPEAGESSTGGP -> PQKTRRKRRSVQN (in isoform 10)

3D Structural Models

Turn
80..82; 104..106; 166..169; 181..183; 367..369
Helix
71..74; 91..93; 293..295
Beta Strand
24..29; 34..36; 43..46; 48..55; 58..60; 62..64; 76..78; 84..88; 95..102; 108..119; 125..128; 131..133; 139..151; 154..159; 162..164; 171..179; 186..194; 206..211; 213..216; 228..230; 237..244; 247..249; 251..253; 255..260; 262..264; 268..273; 284..288; 297..305; 308..312; 316..320; 322..324; 364..366; 371..373
3D Structure
Electron microscopy (1); NMR spectroscopy (10); X-ray crystallography (21)

Domain & Motif Annotations

Compositional Bias
378..396; Acidic residues
Domain (FT)
23..116; Ig-like V-type; 124..221; Ig-like C2-type 1; 227..317; Ig-like C2-type 2
Region
367..404; Disordered
Clinical Relevance
Disease Involvement
Cancer-related genes
Biomarker
Phase 3; Phase 2/3
Drug Targets
Clinical trial target