Protein detail

LRC8C

Volume-regulated anion channel subunit LRRC8C (Factor for adipocyte differentiation 158) (Leucine-rich repeat-containing protein 8C)

Entry name
LRC8C
UniProt ID
EVMP score
0.38
Frequency
6
Transmembrane count
4
Protein classification
Predicted membrane proteinsTransporters
EVMP score: annotation confidence score.
Extremely high >= 0.85High >= 0.70Medium >= 0.55Low >= 0.40
Basic Information
Protein Names
Volume-regulated anion channel subunit LRRC8C (Factor for adipocyte differentiation 158) (Leucine-rich repeat-containing protein 8C)
Protein Class
Predicted membrane proteinsTransporters
Protein Function
Transporters:Transporter channels and pores
Transmembrane
23..47; Helical; Name=1; 125..144; Helical; Name=2; 263..284; Helical; Name=3; 315..339; Helical; Name=4
Transmembrane Count
4
Entrez Gene Symbol
Gene Synonym
AD158
Gene Description
Leucine rich repeat containing 8 VRAC subunit C
Chromosome
1
Position
89633072-89769903
Frequency
6
EVMP Score
0.38
Fluorescence & Localization
Secretome LocationSecreted to bloodSecretome FunctionNo annotated function
Function & Pathway
Relations & Evidence

Enzyme-Mediated Modification

0 records.

Ligand-Receptor Signaling

20 records.

CategoryParentDatabaseTransmitterReceiverSecretedPlasma Membrane (Transmembrane)Plasma Membrane (Peripheral)
transmembranetransmembraneUniProt_locationNoNoNoNoNo
transmembranetransmembraneUniProt_topologyNoNoNoNoNo
transmembranetransmembraneUniProt_keywordNoNoNoNoNo
transmembranetransmembraneTopDBNoNoNoNoNo
transmembranetransmembraneLOCATENoNoNoNoNo
transmembranetransmembraneRamilowski_locationNoNoNoNoNo
transmembranetransmembraneOmniPathNoNoNoNoNo
plasma_membraneplasma_membraneUniProt_locationNoNoNoNoNo
plasma_membraneplasma_membraneOmniPathNoNoNoNoNo
transmembranetransmembrane_predictedPhobiusNoNoNoNoNo
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Regulatory Interaction Network

0 records.

Protein Complex Composition

1 record.

Component NameComponent Gene SymbolsComponent UniProt IDStoichiometryDatabaseDatabase IDsReferences
LRRC8CQ8TDW07PDBPDB:9f16PDB:8dxnPDB:8dxqPDB:8dxoPDB:8dxrPDB:8dxpPDB:8rtsPDB:9ezc

Isolation & Detection Technology

1 record.

EV Isolation MethodDetection MethodNumber of ReferencesReferences
Size Exclusion ChromatographyR SequencingMass spectrometry133749657
Sequence, Structure & Domains

Sequences

Length
803
Mass
92,450
Sequence
MIPVTEFRQFSEQQPAFRVLKPWWDVFTDYLSVAMLMIGVFGCTLQVMQDKIICLPKRVQPAQNHSSLSNVSQAVASTTPLPPPKPSPANPITVEMKGLKTDLDLQQYSFINQMCYERALHWYAKYFPYLVLIHTLVFMLCSNFWFKFPGSSSKIEHFISILGKCFDSPWTTRALSEVSGEDSEEKDNRKNNMNRSNTIQSGPEDSLVNSQSLKSIPEKFVVDKSTAGALDKKEGEQAKALFEKVKKFRLHVEEGDILYAMYVRQTVLKVIKFLIIIAYNSALVSKVQFTVDCNVDIQDMTGYKNFSCNHTMAHLFSKLSFCYLCFVSIYGLTCLYTLYWLFYRSLREYSFEYVRQETGIDDIPDVKNDFAFMLHMIDQYDPLYSKRFAVFLSEVSENKLKQLNLNNEWTPDKLRQKLQTNAHNRLELPLIMLSGLPDTVFEITELQSLKLEIIKNVMIPATIAQLDNLQELSLHQCSVKIHSAALSFLKENLKVLSVKFDDMRELPPWMYGLRNLEELYLVGSLSHDISRNVTLESLRDLKSLKILSIKSNVSKIPQAVVDVSSHLQKMCIHNDGTKLVMLNNLKKMTNLTELELVHCDLERIPHAVFSLLSLQELDLKENNLKSIEEIVSFQHLRKLTVLKLWHNSITYIPEHIKKLTSLERLSFSHNKIEVLPSHLFLCNKIRYLDLSYNDIRFIPPEIGVLQSLQYFSITCNKVESLPDELYFCKKLKTLKIGKNSLSVLSPKIGNLLFLSYLDVKGNHFEILPPELGDCRALKRAGLVVEDALFETLPSDVREQMKTE

3D Structural Models

Turn
283..286; 299..301
Helix
23..48; 107..118; 122..125; 127..143; 153..166; 169..175; 235..253; 260..282; 313..341; 353..358; 369..380; 384..391; 394..404
Beta Strand
52..56; 146..148; 257..259; 289..294; 304..310
3D Structure
Electron microscopy (8)

Domain & Motif Annotations

Compositional Bias
191..209; Polar residues
Repeat
397..420; LRR 1; 421..443; LRR 2; 446..466; LRR 3; 467..488; LRR 4; 490..513; LRR 5; 515..537; LRR 6; 541..563; LRR 7; 565..587; LRR 8; 588..611; LRR 9; 613..635; LRR 10; 636..659; LRR 11; 660..682; LRR 12; 684..705; LRR 13; 706..728; LRR 14; 730..751; LRR 15; 753..774; LRR 16; 776..799; LRR 17
Domain (CC)
The volume-regulated anion channel (VRAC) channel forms a trimer of dimers, with symmetry mismatch between the pore-forming domain and the cytosolic LRR repeats, a topology similar to gap junction proteins.; DOMAIN: The cytoplasmic N-terminus preceding the first transmembrane (residues 1-22) regulates volume-regulated anion channel (VRAC) conductance, ion permeability and inactivation gating.
Region
177..209; Disordered
Protein Families
LRRC8 family
Sequence Similarities
Belongs to the LRRC8 family.
Clinical Relevance
Disease Involvement
Disease variantDwarfismIntellectual disability
Antibody