Protein detail

PYGL

Glycogen phosphorylase, liver form (EC 2.4.1.1)

Protein symbol
PYGL
UniProt ID
EVMP score
0.75
Frequency
34
Transmembrane count
Protein classification
Disease related genesEnzymesHuman disease related genesMetabolic proteinsPlasma proteinsPotential drug targetsPredicted intracellular proteins
Basic Information
Protein Names
Glycogen phosphorylase, liver form (EC 2.4.1.1)
Protein Class
Disease related genesEnzymesHuman disease related genesMetabolic proteinsPlasma proteinsPotential drug targetsPredicted intracellular proteins
Protein Function
  • Human disease related genes:Congenital disorders of metabolism:Congenital disorders of carbohydrate metabolism
  • Predicted intracellular proteins
  • ENZYME proteins:Transferases
  • Potential drug targets
  • Enzymes
  • Disease related genes
Entrez Gene Symbol
Gene Synonym
GSD6
Gene Description
Glycogen phosphorylase L
Chromosome
14
Position
50857891-50944483
Frequency
34
EVMP Score
0.75
Fluorescence & Localization
Cell SpecificB-cellsSingle-Nuclei Brain Specificcentral nervous system macrophage
Function & Pathway
Relations & Evidence

Enzyme-Mediated Modification

3 records.

Substrate Gene SymbolEnzyme Gene SymbolEnzyme UniProt IDResidue TypeResidue OffsetModificationDatabaseReferences
PYGLPHKG2P15735S15phosphorylationSIGNORSIGNOR:22225877
PYGLPHKG1Q16816S15phosphorylationSIGNORSIGNOR:22225877
PYGLOGTO15294S430glycosylationSIGNORSIGNOR:34939084

Ligand-Receptor Signaling

7 records.

CategoryParentDatabaseTransmitterReceiverSecretedPlasma Membrane (Transmembrane)Plasma Membrane (Peripheral)
ecmecmMatrixDBYesNoNoNoNo
ecmecmOmniPathYesNoNoNoNo
extracellularextracellularOmniPathNoNoNoNoNo
intracellularintracellularComPPINoNoNoNoNo
intracellularintracellularGO_IntercellNoNoNoNoNo
intracellularintracellularUniProt_locationNoNoNoNoNo
intracellularintracellularOmniPathNoNoNoNoNo

Regulatory Interaction Network

4 records.

Source Protein SymbolSource UniProt IDTarget Protein SymbolTarget UniProt IDIs DirectedIs StimulationIs InhibitionDatabaseReferences
PHKG1Q16816PYGLP06737YesYesNoiPTMnetSIGNORProtMapperSIGNOR_ProtMapperWangProtMapper:22225877SIGNOR:22225877
OGT1O15294PYGLP06737YesYesNoSIGNORSIGNOR:34939084
RIPK3Q9Y572PYGLP06737YesYesNoInnateDBSIGNORSIGNOR:19632174InnateDB:21903422
PHKG2P15735PYGLP06737YesYesNoiPTMnetSIGNORProtMapperSIGNOR_ProtMapperWangProtMapper:22225877SIGNOR:22225877

Protein Complex Composition

7 records.

Component NameComponent Gene SymbolsComponent UniProt IDStoichiometryDatabaseDatabase IDsReferences
HT_DM_Cluster402MMS19PYGBPYGLPYGMP06737P11216P11217Q96T761:1:1:1CompleatCompleat:HC224522036573
HPRT1MOB1APYGLP00492P06737Q9H8S90:0:0hu.MAP
PYGLP067372PDBPDB:1l7xPDB:2zb2PDB:1l5rPDB:3cehPDB:8emsPDB:1exvPDB:3ddwPDB:1l5qPDB:1xoiPDB:1fc0PDB:2atiPDB:3cejPDB:1l5sPDB:3dd1PDB:3ddsPDB:3cemPDB:1em6
CHORDC1COTL1DUTPITPNBPSAT1PYGLUBE2MP06737P33316P48739P61081Q14019Q9UHD1Q9Y6170:0:0:0:0:0:0hu.MAP2
AGLPYGLP06737P355730:0KEGG-MEDICUS
MOB1AMOB1BPYGLP06737Q7L9L4Q9H8S90:0:0hu.MAP
MOB1APYGLP06737Q9H8S90:0hu.MAP

Isolation & Detection Technology

1 record.

EV Isolation MethodDetection MethodNumber of ReferencesReferences
Differential UltracentrifugationMass SpectrometryWestern Blotting137926697
Sequence, Structure & Domains

Sequences

Length
847
Mass
97,149
Sequence
MAKPLTDQEKRRQISIRGIVGVENVAELKKSFNRHLHFTLVKDRNVATTRDYYFALAHTVRDHLVGRWIRTQQHYYDKCPKRVYYLSLEFYMGRTLQNTMINLGLQNACDEAIYQLGLDIEELEEIEEDAGLGNGGLGRLAACFLDSMATLGLAAYGYGIRYEYGIFNQKIRDGWQVEEADDWLRYGNPWEKSRPEFMLPVHFYGKVEHTNTGTKWIDTQVVLALPYDTPVPGYMNNTVNTMRLWSARAPNDFNLRDFNVGDYIQAVLDRNLAENISRVLYPNDNFFEGKELRLKQEYFVVAATLQDIIRRFKASKFGSTRGAGTVFDAFPDQVAIQLNDTHPALAIPELMRIFVDIEKLPWSKAWELTQKTFAYTNHTVLPEALERWPVDLVEKLLPRHLEIIYEINQKHLDRIVALFPKDVDRLRRMSLIEEEGSKRINMAHLCIVGSHAVNGVAKIHSDIVKTKVFKDFSELEPDKFQNKTNGITPRRWLLLCNPGLAELIAEKIGEDYVKDLSQLTKLHSFLGDDVFLRELAKVKQENKLKFSQFLETEYKVKINPSSMFDVQVKRIHEYKRQLLNCLHVITMYNRIKKDPKKLFVPRTVIIGGKAAPGYHMAKMIIKLITSVADVVNNDPMVGSKLKVIFLENYRVSLAEKVIPATDLSEQISTAGTEASGTGNMKFMLNGALTIGTMDGANVEMAEEAGEENLFIFGMRIDDVAALDKKGYEAKEYYEALPELKLVIDQIDNGFFSPKQPDLFKDIINMLFYHDRFKVFADYEAYVKCQDKVSQLYMNPKAWNTMVLKNIAASGKFSSDRTIKEYAQNIWNVEPSDLKISLSNESNKVNGN
Alternative Products
Event=Alternative splicing; Named isoforms=2; Name=1; IsoId=P06737-1; Sequence=Displayed; Name=2; IsoId=P06737-2; Sequence=VSP_045339
Alternative Sequence
82..115; Missing (in isoform 2)

3D Structural Models

Turn
8..10; 183..186; 342..345; 467..469; 573..576; 635..637; 670..672; 749..751; 756..759
Helix
11..13; 19..38; 44..46; 49..62; 65..78; 96..102; 106..115; 120..125; 136..150; 195..197; 255..260; 263..268; 270..274; 275..277; 291..314; 327..329; 330..333; 346..356; 362..372; 382..384; 390..396; 398..418; 423..429; 442..448; 458..466; 470..475; 477..479; 490..495; 498..508; 511..513; 516..525; 529..553; 577..593; 615..633; 638..640; 651..657; 658..660; 678..684; 697..704; 706..708; 716..725; 729..735; 737..748; 760..768; 774..792; 795..806; 810..812; 814..824
Beta Strand
14..17; 82..86; 90..93; 130..135; 155..160; 168..172; 175..179; 199..204; 206..210; 213..218; 220..232; 234..237; 239..248; 315..317; 322..325; 334..341; 373..376; 387..389; 419..421; 431..433; 435..437; 439..441; 451..457; 480..482; 554..556; 562..569; 595..597; 602..607; 641..646; 662..666; 688..691; 709..711
3D Structure
Electron microscopy (1); X-ray crystallography (18)

Domain & Motif Annotations

Protein Families
Glycogen phosphorylase family
Sequence Similarities
Belongs to the glycogen phosphorylase family.
Clinical Relevance
Disease Involvement
Disease variantGlycogen storage disease
Interaction Protein
ENSG00000096060ENSG00000100994
Interaction Count
2
Interaction Dataset
biogrid_opencellintact_biogrid_bioplex