Protein detail

PRRT2

Proline-rich transmembrane protein 2 (Dispanin subfamily B member 3) (DSPB3)

Protein symbol
PRRT2
UniProt ID
EVMP score
0.50
Frequency
5
Transmembrane count
1
Protein classification
Disease related genesHuman disease related genesPotential drug targetsPredicted intracellular proteinsPredicted membrane proteinsTransporters
Basic Information
Protein Names
Proline-rich transmembrane protein 2 (Dispanin subfamily B member 3) (DSPB3)
Protein Class
Disease related genesHuman disease related genesPotential drug targetsPredicted intracellular proteinsPredicted membrane proteinsTransporters
Protein Function
  • Human disease related genes:Nervous system diseases:Other nervous and sensory system diseases
  • Predicted intracellular proteins
  • Human disease related genes:Nervous system diseases:Epilepsy
  • Potential drug targets
  • Transporters:Accessory Factors Involved in Transport
  • Disease related genes
Transmembrane
318..338; Helical
Transmembrane Count
1
Entrez Gene Symbol
Gene Synonym
DKFZp547J199DSPB3DYT10EKD1FICCAFLJ25513ICCAIFITMD1PKC
Gene Description
Proline rich transmembrane protein 2
Chromosome
16
Position
29811382-29815892
Frequency
5
EVMP Score
0.50
Fluorescence & Localization
Tissue SpecifickidneyCell SpecificRenal collecting duct intercalated cellsSingle-Nuclei Brain Specificmammillary body
Function & Pathway
Protein Function
  • Human disease related genes:Nervous system diseases:Other nervous and sensory system diseases
  • Predicted intracellular proteins
  • Human disease related genes:Nervous system diseases:Epilepsy
  • Potential drug targets
  • Transporters:Accessory Factors Involved in Transport
  • Disease related genes
Mediation Categories
Fusion and delivery mediationReceptor-signaling mediation
Relations & Evidence

Enzyme-Mediated Modification

0 records.

Ligand-Receptor Signaling

14 records.

CategoryParentDatabaseTransmitterReceiverSecretedPlasma Membrane (Transmembrane)Plasma Membrane (Peripheral)
peripheralperipheralOmniPathNoNoNoNoNo
plasma_membraneplasma_membraneUniProt_locationNoNoNoNoNo
plasma_membraneplasma_membraneOmniPathNoNoNoNoNo
transmembranetransmembrane_predictedPhobiusNoNoNoNoNo
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Regulatory Interaction Network

0 records.

Protein Complex Composition

0 records.

Isolation & Detection Technology

1 record.

EV Isolation MethodDetection MethodNumber of ReferencesReferences
Mass spectrometry0
Sequence, Structure & Domains

Sequences

Length
340
Mass
34,945
Sequence
MAASSSEISEMKGVEESPKVPGEGPGHSEAETGPPQVLAGVPDQPEAPQPGPNTTAAPVDSGPKAGLAPETTETPAGASETAQATDLSLSPGGESKANCSPEDPCQETVSKPEVSKEATADQGSRLESAAPPEPAPEPAPQPDPRPDSQPTPKPALQPELPTQEDPTPEILSESVGEKQENGAVVPLQAGDGEEGPAPEPHSPPSKKSPPANGAPPRVLQQLVEEDRMRRAHSGHPGSPRGSLSRHPSSQLAGPGVEGGEGTQKPRDYIILAILSCFCPMWPVNIVAFAYAVMSRNSLQQGDVDGAQRLGRVAKLLSIVALVGGVLIIIASCVINLGVYK
Alternative Products
Event=Alternative splicing; Named isoforms=3; Name=1; IsoId=Q7Z6L0-1; Sequence=Displayed; Name=2; IsoId=Q7Z6L0-2; Sequence=VSP_028815; Name=3; IsoId=Q7Z6L0-3; Sequence=VSP_028814
Alternative Sequence
294..340; SRNSLQQGDVDGAQRLGRVAKLLSIVALVGGVLIIIASCVINLGVYK -> VSPMGP (in isoform 3); 337; G -> GGEWGLGTGRGGMEGLARAALLTPAPALSCLSSLPLLCLSLSPPPPVCPSLSSPT (in isoform 2)

3D Structural Models

Domain & Motif Annotations

Compositional Bias
9..18; Basic and acidic residues; 131..155; Pro residues; 197..207; Pro residues
Region
1..261; Disordered
Protein Families
CD225/Dispanin family
Sequence Similarities
Belongs to the CD225/Dispanin family.
Clinical Relevance
Disease Involvement
Disease variantDystoniaEpilepsy